Ixesha lokufunda eliqikelelweyo: 5 mzuzu
Table of Contents
Yintoni i-Supravalvular Mitral Valve Obstruction?
I-Supravalvular Mitral Valve Obstruction (SMI) yimeko apho kukho umqobo wokuhamba kwegazi ukuya kwi-ventricle yasekhohlo yentliziyo. Esi sithintelo sithintela ukuhamba kwegazi phakathi kwe-atrium yasekhohlo kunye ne-ventricle yasekhohlo. Oku kubangela ukuba intliziyo isebenze nzima ukumpompa igazi.
Ezi ntlobo zokuvala zinqabile kwaye ubukhulu becala umsesane we-supramitral (SMR) okanye icor triatriatum sinister (CTS) Inxulunyaniswa nezinto ezimbini ezingaqhelekanga ezibizwa ngokuba . Nangona iziphumo kunye neempawu zeklinikhi zezi meko zimbini emzimbeni zifana, izizathu zabo kunye nezakhiwo zihlukile.
Umahluko phakathi kweSupramitral Ring (SMR) kunye neCor Triatriatum Sinister (CTS)
• IRingi yeSupramitral (SMR)Kule meko, i-ring of tissue ikhula ngaphakathi kwe-atrium yasekhohlo, ngaphezu kwevalve ye-mitral. Le ringi inqanda ukuhamba kwegazi ukusuka kwi-atrium yasekhohlo ukuya kwi-ventricle yasekhohlo.
• Cor Triatriatum Sinister (CTS)Kule meko, i-atrium yasekhohlo ibekwe ngokuthe tye inwebu ye-fibromuscular Yahlulwe ngamagumbi amabini ahlukeneyo ngevalve ye-mitral. Le inwebu ithintela ukuba igazi lingadluleli kakuhle kwivalve ye-mitral.
Kuzo zombini ezi meko, kwi-atrium yasekhohlo ukuhamba kwegazi kuyehla kunye nentliziyo ukumpompa igazi elaneleyo kuwo wonke umzimba kufuneka asebenze nzima.
Ibonwa Kweziphi Iintlanga?
Ezi meko zinqabile kuzo zombini izinja neekati. Nangona kunjalo, kwiikati Kuye kwaxelwa rhoqo. Nangona kunjalo, akukho ngcaciso ecacileyo malunga nokuba yiyiphi inzala yekati okanye inja ethandwa kakhulu kwesi sifo.
Ziziphi iimpawu?
Iimpawu zokuphazamiseka kwevalve ye-supramitral zixhomekeke kwiqondo lothintelo kunye nenqanaba apho ukuphuma kwegazi kuthintelwe. Ukuba isithintelo sincinci, isilwanyana sinokungabonakali naziphi na iimpawu. Nangona kunjalo, ukuba isithintelo sinzima, iimpawu ziya kubonakala ngakumbi.
Iimpawu ezinokwenzeka ziquka:
• Ukuqhawukelwa ngumphefumlo: Ukuqokelelwa kolwelo emiphungeni (i-pulmonary edema) ingenzeka ngenxa yokuxhaswa kwegazi kwimiphunga.
• Ziqhelise ukunganyamezeliIsilwanyana sinokudinwa ngokukhawuleza kwaye sizive sifuna ukuphumla.
• ukuphefumla ngokukhawuleza: Ukuphefumla ngokukhawuleza kunokwenzeka ngenxa yokwanda kolwelo emiphungeni.
• KhohlelaUkukhohlela kungenzeka ezinjeni nasezikatini, ngakumbi xa kukho ukufumba kolwelo emiphungeni.
Iimpawu zibangelwa ligazi elibuyela emiphungeni. ukuxinana kwemiphunga (uxinzelelo olongezelelweyo kwiinqanawa ze-pulmonary).
I-Supravalvular Mitral Valve ixilongwa njani?
Ukufumanisa ukuvaleka kwevalve ye-supramitral kunokuba nzima kuba iimpawu zolu hlobo lungaqhelekanga zinokufana nezo zezinye iimeko zentliziyo.
1. Uvavanyo loMzimba
Ugqirha wezilwanyana umamela intliziyo ngestethoscope Ukumbombozela (isandi esingaqhelekanga sentliziyo) Noko ke, oku kumbombozela kusenokungabonakali lula njengokuba kusenzeka ebantwini.
2. X-reyi (iRadiyografi)
Imifanekiso ye-X-reyi inokubonisa intliziyo eyandisiweyo (ingakumbi i-atrium yasekhohlo) kunye nokwanda kolwelo emiphungeni. Oku kubonakala ngokukodwa xa i-atrium yasekhohlo yandiswa, idala isithunzi esikhulu kuloo ndawo kwi-X-reyi yesifuba.
3. I-Echocardiography (i-Heart Ultrasound)
I-cardiac ultrasound yeyona ndlela isebenzayo yokuxilonga esi sifo. I-Ultrasound ivumela umbono ocacileyo wesakhiwo sentliziyo kunye nokuhamba kwegazi. Ugqirha wezilwanyana, ukuba i-atrium yasekhohlo yahlulwe ngamagumbi amabini okanye umsesane we-supramitral inokuvavanya ngale mifanekiso ukuba yiyo okanye hayi.
• Umbala weDoppler ultrasound: Isetyenziselwa ukubonisa ukuba leliphi icala kwaye igazi lihamba ngokukhawuleza kangakanani.
• I-Doppler yamaza eqhubekayo: Imisela iqondo lothintelo ngokulinganisa umahluko woxinzelelo kunye nesantya sokuhamba kwegazi.
Ingaba iSupravalvular Mitral Valve iNyangwa njani?
Unyango lwesi sifo luxhomekeke kubuzaza bothintelo kunye nempilo yesilwanyana ngokubanzi.
1. Unyango lweziyobisi
Unyango lweziyobisi aluphelisi ingcambu yesi sifo, kodwa ivumela isilwanyana ukuba siphefumle ngokulula kwaye iingxaki ezinzima ilawula.
• i-diuretics: Inceda ukususa ulwelo olugqithisileyo oluqokelelwe emiphungeni.
• Unyango lweoksijini: Isetyenziselwa ukunciphisa ukuphefumla kancinci ngexesha lohlaselo oluqatha.
2. Unyango lotyando
Kwiimeko zokuthintela kakhulu, ukungenelela ngotyando kunokufuneka. Utyando lwe-Cardiopulmonary bypass (CPB) okanye utyando oluxutyiweyo Oku kuthinteleka kunokususwa ngobuchule obukhethekileyo botyando obubizwa ngokuba.
• Cor Triatriatum Sinister (CTS) utyandoKule meko, i-membrane eyahlula i-atrium ekhohlo kubini ingandiswa okanye inqunywe ngoncedo lwebhaluni ekhethekileyo.
• Supramitral Ring (SMR) utyandoKule meko, ekubeni isithintelo sisondele kwi-valve ye-mitral, ukungenelela kokuhlinzwa kuyadingeka. ingozi yomonakalo kwivalve ye-mitral Ngoko ke, oogqirha bezilwanyana kufuneka bacwangcise utyando ngononophelo olukhulu.
Yintoni Ukubaluleka Kwesi Sifo?
Nangona i-supramitral valve obstruction isisifo esingaqhelekanga, sinokuchaphazela kakhulu umgangatho wobomi besilwanyana. Ukuxilongwa kwangoko Imiphumo yesi sifo ingancitshiswa kakhulu ngale ndlela. Ugqirha wezilwanyana usebenzisa iimvavanyo ezahlukeneyo ukufumanisa ukuxilongwa kunye nesicwangciso sonyango. Ngokukodwa, i-echocardiographyibaluleke kakhulu ekuxilongeni izifo zentliziyo ezinqabileyo ngolo hlobo.
Isilwanyana esinale meko kufuneka sibekwe iliso elibukhali ngokuhlolwa rhoqo kugqirha wezilwanyana. Ukuba iimpawu ziba mandundu, kubalulekile ukuba uqhagamshelane nogqirha wakho wezilwanyana ngokukhawuleza.
Amanye amanqaku onokuthi ube nonomdla kuwo
"Ukufunda kusenokubiza, kodwa ukungazi kubiza kakhulu."
UClaus Moser