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Supravalvular Mitral Valve Obstruction

Manaʻo manawa heluhelu: 5 minuke

Transthoracic echocardiogram e hōʻike ana i ke apo supramitral, subaortic membrane, dilated coronary sinus a me ka mitral inflow obstruction.AO: Aorta, LA a me RA: Left and right atrium, LV and RV: Left and right ventricle

He aha ka Supravalvular Mitral Valve Obstruction?

ʻO ka Supravalvular Mitral Valve Obstruction (SMI) kahi ʻano keakea i ke kahe ʻana o ke koko i ka ventricle hema o ka puʻuwai. Hoʻopaʻa ʻia kēia keakea i ke kahe koko ma waena o ka atrium hema a me ka ventricle hema. ʻO kēia ka mea e hoʻoikaika nui ai ka puʻuwai e paʻi i ke koko.

ʻAʻole kakaikahi kēia mau ʻano paʻa a ʻo ka hapa nui apo kiʻekiʻe (SMR) ai ole ia, cor triatriatum sinister (CTS) Hoʻopili ʻia me ʻelua mau mea ʻino i kapa ʻia . ʻOiai ua like nā hopena a me nā hōʻailona lapaʻau o kēia mau kūlana ʻelua i ke kino, ʻokoʻa nā kumu a me nā ʻano.


Nā ʻokoʻa ma waena o Supramitral Ring (SMR) a me Cor Triatriatum Sinister (CTS)

apo kiʻekiʻe (SMR)Ma kēia kūlana, ulu ka apo o ka ʻiʻo i loko o ka atrium hema, ma luna pono o ka valve mitral. Mālama kēia apo i ke kahe o ke koko mai ka atrium hema a i ka ventricle hema.

Cor Triatriatum Sinister (CTS)I kēia hihia, ʻo ka atrium hema he pae hoʻonohonoho fibromuscular membrane Hoʻokaʻawale ʻia ia i ʻelua keʻena kaʻawale e ka mitral valve. Mālama kēia membrane i ke kahe ʻana o ke koko mai ka hele mālie ʻana ma o ka valve mitral.

I nā hihia ʻelua, ma ka atrium hema lohi ke kahe o ke koko a me ka puʻuwai e pāpaʻi i ke koko ma ke kino pono e hana ikaika.


Ma na heihei hea i ike ia ai?

He kakaikahi kēia mau kūlana i nā ʻīlio a me nā pōpoki. Eia naʻe, i nā pōpoki Ua hōʻike pinepine ʻia. Eia nō naʻe, ʻaʻohe ʻike maopopo e pili ana i nā ʻīlio a i ʻole nā ​​​​ʻīlio i ʻoi aku ka maʻi i kēia maʻi.


He aha nā hōʻailona?

ʻO nā hōʻailona o ke kīpē supramitral e pili ana i ke kiʻekiʻe o ke keakea a me ke ʻano o ke kahe ʻana o ke koko. Inā liʻiliʻi ka mea keakea, ʻaʻole hōʻike ka holoholona i nā hōʻailona. Eia naʻe, inā paʻakikī ke keʻakeʻa, e ʻoi aku ka nui o nā hōʻailona.

Aia nā hōʻailona hiki ke:

Pokole o ka hanu: Hiki ke hoʻonui ʻia ka wai i loko o ka māmā (pulmonary edema) ma muli o ke kākoʻo ʻana o ke koko i loko o ka māmā.

E hoʻokō i ka hoʻomanawanuiHiki i ka holoholona ke luhi wikiwiki a manaʻo ka pono e hoʻomaha.

hanu wikiwiki: Hiki ke hanu wikiwiki ma muli o ka hōʻiliʻili ʻana o ka wai i loko o ka māmā.

ʻAhuHiki i nā ʻīlio a me nā pōpoki ke ʻāʻī, ʻoi aku ka nui o ka loaʻa ʻana o ka wai i loko o ka māmā.

Loaʻa nā hōʻailona ma muli o ke kahe hou ʻana o ke koko i loko o ka māmā. puʻupuʻu puʻupuʻu (hoʻonui i ke kaomi i loko o nā moku pulmonary).


Pehea ʻo Supravalvular Mitral Valve Obstruction i ʻike ʻia?

Hiki ke paʻakikī ka ʻike ʻana i ka ʻākeʻa ʻana o ka valve supramitral no ka mea hiki ke ʻano like nā hōʻailona o kēia ʻano ʻino me nā maʻi ʻē aʻe o ka naʻau.

1. Nānā kino

Hoʻolohe ka mea lapaʻau i ka puʻuwai me kahi stethoscope ʻōhumu (ke kani puʻuwai ʻole) Akā naʻe, ʻaʻole hiki ke ʻike maʻalahi kēia ʻōhumu e like me ke kanaka.

2. X-ray (Radiography)

Hōʻike paha nā kiʻi X-ray i ka puʻuwai i hoʻonui ʻia (ʻoi aku ka atrium hema) a me ka hōʻiliʻili wai i loko o ka māmā. ʻIke ʻia kēia i ka wā e hoʻonui ʻia ai ka atrium hema, e hana ana i kahi aka nui ma ia wahi ma ka pahu X-ray.

3. Echocardiography (Naʻau Ultrasound)

ʻO ka ultrasound cardiac ke ala kūpono loa no ka ʻike ʻana i kēia maʻi. Hiki i ka Ultrasound ke ʻike maopopo i ke ʻano o ka puʻuwai a me ke kahe koko. ʻO ke kauka holoholona, ina paha ua maheleia ka atrium hema i elua keena ai ole ia, apo supramitral hiki ke loiloi me kēia mau kiʻi inā ʻaʻole paha.

ʻO ke kala kala Doppler ultrasound: Hoʻohana ʻia e hōʻike i ka ʻaoʻao hea a me ka wikiwiki o ke kahe ʻana o ke koko.

Doppler nalu mau: Hoʻoholo i ke kiʻekiʻe o ke keakea ma ke ana ʻana i ka ʻokoʻa kaomi a me ka wikiwiki o ke kahe koko.


Pehea ka mālama ʻia ʻana o Supravalvular Mitral Valve Obstruction?

ʻO ka mālama ʻana i kēia maʻi ma muli o ke ʻano o ke keʻakeʻa a me ke olakino holoʻokoʻa o ka holoholona.

1. Laau Laau Laau

ʻAʻole hoʻopau ka lāʻau lapaʻau i ke kumu kumu o kēia maʻi, akā hiki i ka holoholona ke hanu maʻalahi a maʻalahi pilikia nui hooponopono.

diuretics: Kōkua ia e wehe i ka wai nui i hōʻiliʻili ʻia i loko o ka māmā.

ʻO ka lāʻau lapaʻau: Hoʻohana ʻia e hōʻemi i ka pōkole o ka hanu i ka wā o ka hoʻouka ʻana.

2. Lapaau Opuu

I nā hihia o ke keakea nui, pono paha ke kaʻina hana. ʻO ke kāʻei ʻana i ka puʻuwai puʻuwai (CPB) a i ʻole ʻokiʻoki hybrid Hiki ke hoʻoneʻe ʻia kēia poloka me kahi ʻano hana ʻoki kūikawā i kapa ʻia.

ʻO ka ʻoki ʻana o Cor Triatriatum Sinister (CTS).I kēia hihia, hiki ke hoʻonui a ʻoki ʻia ka membrane e hoʻokaʻawale i ka atrium hema i ʻelua me ke kōkua o kahi baluna kūikawā.

Hoʻokiʻoki ʻia ke apo Supramitral (SMR).Ma keia hihia, no ka mea, ua kokoke ke keakea i ka mitral valve, pono ke kaupa'i. pilikia i ka pōʻino o ka pahu mitral No laila, pono e hoʻolālā nā kauka lāʻau lapaʻau i ke kaʻina me ke akahele loa.


He aha ke koʻikoʻi o kēia maʻi?

ʻOiai he maʻi kakaʻikahi ka hoʻopaʻa ʻana o ka valve supramitral, hiki ke hoʻopilikia koʻikoʻi i ka maikaʻi o ke ola o ka holoholona. ʻIke mua Hiki ke hoʻemi nui ʻia nā hopena o kēia maʻi me kēia ʻano hana. Hoʻohana ka mea lapaʻau i nā hoʻokolohua like ʻole e hoʻoholo ai i ka maʻi a me ka hoʻolālā lapaʻau. ʻOiaʻiʻo, echocardiographyHe mea koʻikoʻi loa ia i ka ʻike ʻana i ia mau maʻi puʻuwai kakaʻikahi.

Pono e nānā pono ʻia kahi pipi me kēia maʻi me ka nānā ʻana i nā holoholona holoholona. Inā ʻoi aku ka nui o nā hōʻailona, ​​​​pono e hoʻopili koke i kāu kauka holoholona.


Pehea ʻoe i ʻike ai i ka ʻatikala?
E noʻonoʻo ʻia kāu mau loiloi ma kēia ʻāpana akā ʻaʻole e paʻi ʻia.
Ua manaʻo paha ʻoe he mea pono ka ʻike?


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